Correction and stabilization of spinal deformities in patients with systemic skeletal diseases
Objective. To analyze the effect of developed methods of diagnosis and treatment on the improvement of outcomes in patients with secondary spinal deformities associated with hereditary systemic skeletal diseases. Material and Methods. The treatment experience of 36 patients with spinal deformity associated with hereditary systemic skeletal disease is presented. Individual diseases causing secondary scoliosis are characterized. The algorithm of examination and tactics of these patients are presented. Particularities of posterior, anterior, and multifunction surgical approaches are described. Results. The use of combined approaches and new instrumentation provides good outcomes in patients with spinal deformities associated with hereditary systemic skeletal diseases. The mean deformity angle before operation was 105 degrees, after operation - 47 degrees. Mean correction in the postoperative period reached 56 %. Conclusion. Wide introduction of the modern segmental instrumentation allowing for multiplane correction of spine deformity along side with application of anterior, posterior, and combined approaches, as well as cooperation of specialists in hereditary systemic skeletal diseases and specialists in spine medicine provide good outcomes in these patients.