Juvenile systemic scleroderma: clinical presentation and modern approaches to treatment (clinical case)
Systemic scleroderma is a rare autoimmune disease, which affects the skin, musculoskeletal system, gastrointestinal tract, cardiovascular and respiratory systems. The article highlights the pathogenesis of systemic scleroderma in children, clinical manifestations, diagnostic features, and modern recommendations for treatment of this pathology. The effects of burden anamnesis, late diagnostics and initiation of therapy, the questions of differential diagnostics are considered on the example of the clinical case of systemic scleroderma in a child. There is highlighted the management tactics with the possibility of improvement of the quality of life and long-term prognosis. In conclusion,it is noted that systemic scleroderma is a multidisciplinary problem, and it can be interested for physicians of many specialties.