DIAGNOSTIC AND MANAGEMENT OF PULMONARY ARTERIAL HYPERTENSION ASSOCIATED WITH CONGENITAL HEART DISEASES IN CHILDREN
Pulmonary arterial hypertension associated with congenital heart disease (APAH-CHD) is a formidable and common complication in half of the cases with the natural course of congenital system-to-pulmonary shunts. According to international national registers the incidence of APAH-CHD varies from 11.3 to 15.6 cases per million of population. Most of the international expert centres studies the aspects of pulmonary arterial hypertension in the adult population. Pediatric practice is faced with a lack of knowledge and experience about this pathology in childhood. We have reviewed the literature on pulmonary arterial hypertension associated with congenital heart disease in paediatric practice. This publication is part of a doctoral dissertation and continues the review on this specific topic.